Objective: This paper describes functional impairments experienced by children with Cortical/Cerebral Visual Impairment (CVI) and how occupational therapists (OTs) play an important role in the evaluation of functional vision and intervention guided by the Person-Environment-Occupation (PEO) model. Background: Prevalence of CVI in children is increasing; however, there is lack of consensus on diagnostic practices and few studies evaluating interventions for children with CVI. Some papers discuss the difficulties children with CVI experience in areas such as self-care, play, education, and mobility, but there is minimal evidence to support OT efforts. Methods: A narrative literature review was conducted to identify relevant research. A comprehensive search was performed across multiple databases. Studies that met the inclusion criteria were synthesized for key findings. Discussion: Findings supported that children with CVI face challenges with functional vision impacting daily living skills. These daily skills fall within the OT scope of practice. Although evidence-based interventions specific to OT are limited for CVI, existing literature reports deficits in ADLs, IADLs, play, education, and social participation, emphasizing the need for OT specific interventions for children with CVI. Conclusion: Due to OT’s focus on daily activities (occupations), environmental and activity modification, and emphasis on client-specific care, they have a distinct role in caring for this population.